Atrial Flutter and Myotonic Dystrophy in a Male Adolescent Treated With Radiofrequency Catheter Ablation
Document Type
Review
Publication Date
3-1-2007
Description
A variety of cardiomyopathies are due to familial disease. Most are primarily associated with cardiac involvement and can lead to hypertrophic, dilated, or restrictive cardiomyopathy. Myotonic dystrophy (MD) is a multisystem disease with autosomal dominant inheritance and variable penetrance. Cardiac diseases are important causes of morbidity and mortality in MD patients. Patients with primary MD should be carefully investigated with an electrocardiogram, stress test, and an echocardiogram to identify preclinical cardiac involvement and to prevent life-threatening complications. Any new onset of atrial flutter or atrial fibrillation in a young patient without any underlying cardiac abnormality should be investigated for underlying myopathy. The authors report on a male adolescent with MD who presented with atrial flutter. The patient had been diagnosed with MD at birth. He had an impaired ejection fraction of 38% to 45%. The patient described sharp chest pain in the retrosternal area, with no radiation, that was induced by exercise.
Citation Information
Halawa, Ahmad; Iskandar, Said B.; Brahmbhatt, Vipul; and Fahrig, Stephen A.. 2007. Atrial Flutter and Myotonic Dystrophy in a Male Adolescent Treated With Radiofrequency Catheter Ablation. Reviews in Cardiovascular Medicine. Vol.8(2). 118-122. https://pubmed.ncbi.nlm.nih.gov/17603429/ PMID: 17603429 ISSN: 1530-6550